Aortic root dilatation associated with partial trisomy 7(q31.2→qter)
نویسندگان
چکیده
منابع مشابه
Aortic Root Dilatation in Mucopolysaccharidosis I–VII
The prevalence of aortic root dilatation (ARD) in mucopolysaccharidosis (MPS) is not well documented. We investigated aortic root measurements in 34 MPS patients at the Children's Hospital of Orange County (CHOC). The diagnosis, treatment status, age, gender, height, weight and aortic root parameters (aortic valve annulus (AVA), sinuses of Valsalva (SoV), and sinotubular junction (STJ)) were ex...
متن کاملThe extent of the raphe in bicuspid aortic valves is associated with aortic regurgitation and aortic root dilatation
BACKGROUND The clinical course of bicuspid aortic valves (BAVs) is variable. Data on predictors of aortopathy and valvular dysfunction mainly focus on valve morphology. AIM To determine whether the presence and extent of the raphe (fusion site of valve leaflets) is associated with the degree of aortopathy and valvular dysfunction in patients with isolated BAV and associated aortic coarctation...
متن کاملValve-sparing aortic root replacement and aortic valve repair in a patient with acromegaly and aortic root dilatation
Aortic regurgitation and dilatation of the aortic root and ascending aorta are severe complications of acromegaly. The current trend for management of an aortic root aneurysm is valve-sparing root replacement as well as restoring the diameter of the aortic sinotubular junction (STJ) and annulus. Our case report supports the recommendation that in patients with acromegaly, severe aortic root inv...
متن کاملSurgical Management of Aortic Root Dilatation with Advanced Aortic Regurgitation: Bentall Operation versus Valve-sparing Procedure
BACKGROUND Although the aortic valve-sparing procedure has gained popularity in recent years, it still remains challenging in patients with advanced aortic regurgitation (AR). We compared the long-term outcomes of the aortic valve-sparing procedure with the Bentall operation in patients with advanced aortic regurgitation secondary to aortic root dilatation. MATERIALS AND METHODS A retrospecti...
متن کاملAortic root dilatation in young men with normally functioning bicuspid aortic valves.
OBJECTIVE To evaluate the dimensions of the aortic root in a selected population of young males with isolated normally functioning bicuspid aortic valve. DESIGN AND SETTING Echocardiographic and Doppler evaluation of conscripts with bicuspid aortic valve at the time of military pre-enrolment screening in two military hospitals. SUBJECTS AND METHODS 66 consecutive young men with a normally f...
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ژورنال
عنوان ژورنال: Pediatric Cardiology
سال: 1989
ISSN: 0172-0643,1432-1971
DOI: 10.1007/bf02328637